CONGENITAL CYSTIC ADENOMATOID MALFORMATION OF THE LUNGS: A CASE REPORT
DOI:
https://doi.org/10.53582/a97qr940Keywords:
newborn, congenital cystic adenomatoid malformationsAbstract
Congenital cystic adenomatoid malformations (CCAM) of the lung are a rare congenital disorder. The prevalence of this condition is 9 per 100,000 births, with a slight predominance in males. Most cases present clinically in the neonatal period, but may remain asymptomatic until adulthood. The etiology of CCAM is not fully understood. Fetal cystic changes of the lungs are detected prenatally by ultrasound, and postnatally, the definitive method is chest computed tomography (CT) or magnetic resonance imaging (MRI). Resection of CCAM is recommended due to the risk of malignancy. We present the case of a term-male hypotrophic newborn, in whom cystic changes of the right lung were detected prenatally. The chest X-ray and CT scan postnatally confirmed right-sided congenital adenomatoid cysts. At the age of 2 months, the infant underwent surgical resection of cystic changes, and CCAM type 1 was histologically proven.
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